Q J Med 1990; 74: 63-74
© 1990 Association of Physicians
other |
Outcome of End-stage Renal Disease in Patients with Rare Causes of Renal Failure. III. Systemic/Vascular Disorders
UCLA School of Medicine 10833 Le Conte Avenue, 57-143 CHS, Los Angeles, CA 90024 Hemodialysis Unit, University of Michigan Medical School, Veterans Administration Medical Center 2215 Fuller Road, Ann Arbor, Michigan 48105, U.S.A.
Address correspondence to Dr Nissenson
Accepted for publication 6 June 1989.
This multicentre national study has provided demographic and outcome data on over 1700 patients with rare systemic/vascular diseases as a cause of ESRD [1]. Except for those with Henoch-Schönlein purpura, polyarteritis nodosa and Wegener's granulomatosis, women predominated. On the other hand, black patients seem less susceptible to these illnesses than white patients except for SLE. Recovery of renal function sufficient for dialysis to be discontinued was more likely in each of these diseases except for SLE than for any of the other ‘rare’ diseases described by us [2, 3], the usual causes of renal failure as reported by the EDTA Registry [12] or our control patients. Overall survival was quite good except in those patients with progressive systemic sclerosis whose outlook was poor.