Skip Navigation

This Article
Right arrow Full Text (PDF)
Right arrow Alert me when this article is cited
Right arrow Alert me if a correction is posted
Services
Right arrow Email this article to a friend
Right arrow Similar articles in this journal
Right arrow Similar articles in PubMed
Right arrow Alert me to new issues of the journal
Right arrow Add to My Personal Archive
Right arrow Download to citation manager
Right arrowRequest Permissions
Right arrow Disclaimer
Google Scholar
Right arrow Articles by MCGONIGLE, R. J. S.
Right arrow Articles by PARSONS, V.
Right arrow Search for Related Content
PubMed
Right arrow PubMed Citation
Right arrow Articles by MCGONIGLE, R. J. S.
Right arrow Articles by PARSONS, V.
Social Bookmarking
Add to CiteULike   Add to Connotea   Add to Del.icio.us  
What's this?

Q J Med 1981; 50: 269-278
© 1981 Association of Physicians

research-article

Congenital Hepatic Fibrosis and Polycystic Kidney Disease; Role of Porta-Caval Shunting and Transplantation in Three Patients

RICHARD J. S. MCGONIGLE, ALEX P. MOWAT, MICHAEL BEWICK, EDWARD R. HOWARD, SUSAN A. SNOWDEN and VICTOR PARSONS

From the Departments of Renal Medicine, Surgery and Child Health, King's College Hospital Denmark Hill, London, SE5

Accepted for publication 2 February 1981.

Three patients with congenital hepatic fibrosis and childhood-type autosomal recessive polycystic kidney disease are reported. Portal hypertension in two of the children was decompressed surgically by lieno-renal shunting, and the renal failure in two children has been successfully treated with renal transplantation. Prophylactic porta-caval shunting followed by renal transplantation is ideally suited to the sequence of events occurring clinically in the intermediate form of this condition, preventing complications of bleeding from oesophageal varices and hypersplenism. The relationship of congenital hepatic fibrosis with the various forms of polycystic kidney disease is discussed and classified.


Add to CiteULike CiteULike   Add to Connotea Connotea   Add to Del.icio.us Del.icio.us    What's this?




Disclaimer: Please note that abstracts for content published before 1996 were created through digital scanning and may therefore not exactly replicate the text of the original print issues. All efforts have been made to ensure accuracy, but the Publisher will not be held responsible for any remaining inaccuracies. If you require any further clarification, please contact our Customer Services Department.